Rabbit Polyclonal Antibody to OTC
货号:
P23093
别名:
OTCase; Ornithine carbamoyltransferase; mitochondrial; OCTD
应用:
WB,IP,IHC
反应种属:
Mouse,Rat
抗体类型:
Primary antibody
Swissprot:
P00480
规格:
目录价
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Description |
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This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. |
Specification |
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Aliases | OTCase; Ornithine carbamoyltransferase; mitochondrial; OCTD |
Entrez GeneID | 5009 |
Swissprot | P00480 |
WB Predicted band size | Calculated MW: 40 kDa; Observed MW: 40 kDa |
Host/Isotype | Rabbit IgG |
Antibody Type | Primary antibody |
Storage | Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles. |
Species Reactivity | Mouse,Rat |
Immunogen | A synthetic peptide of human Ornithine Carbamoyltransferase |
Formulation | Purified antibody in TBS with 0.05% sodium azide,0.05%BSA and 50% glycerol. |
Application |
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WB | 1/500-1/1000 |
IP | 1/10-1/20 |
IHC | 1/50-1/100 |