Rabbit Polyclonal Antibody to GNS
货号:
P10451
别名:
G6S
应用:
WB,IHC
反应种属:
Human, Mouse
抗体类型:
Primary antibody
Swissprot:
P15586
规格:
目录价
在线咨询
Description |
---|
The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. |
Specification |
|
---|---|
Aliases | G6S |
Swissprot | P15586 |
WB Predicted band size | 62 kDa |
Host/Isotype | Rabbit IgG |
Antibody Type | Primary antibody |
Storage | Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles. |
Species Reactivity | Human, Mouse |
Immunogen | Fusion protein of human GNS |
Formulation | Purified antibody in PBS with 0.05% sodium azide and 50% glycerol. |
Application |
|
---|---|
WB | 1/500-1/2000 |
IHC | 1/50-1/200 |
ELISA | 1/5000-1/10000 |
Product Image
-
Gel: 8%SDS-PAGE, Lysate: 40 μg, Lane: PC3 cell lysate, Primary antibody: P10451(GNS Antibody) at dilution 1/700, Secondary antibody: Goat anti rabbit IgG at 1/5000 dilution, Exposure time: 1 minute
-
The image is immunohistochemistry of paraffin-embedded Human cervical cancer tissue using P10451(GNS Antibody) at dilution 1/80. (Original magnification: ×200)
-
The image is immunohistochemistry of paraffin-embedded Human colorectal cancer tissue using P10451(GNS Antibody) at dilution 1/80. (Original magnification: ×200)